Double Inlet Left Ventricle (DILV), Double Outlet Left Ventricle (DOLV), Malposition of Great Arteries, Inlet Ventricle Septal Defect (VSD) and Patent Ductus Arteriosus
AbstractCongenital heart disease is an interesting area which present a great various arrangement of the cardiac stucture. We present a rare case of 11 months old male with complex congenital heart disease consisted of Double Inlet Left Ventricle (DILV), Double Outlet Left Ventricle (DOLV) with Malposition of Great Arteries, Inlet Ventricle Septal Defect (VSD) and Patent Ductus Arteriosus (PDA).Patient was an eleven months old male who was admitted in our institution for cardiac operation. He was diagnosed with congenital heart disease since three days old with initial presentation of cyanosis when he was crying. His physical growth was retarded but his developmental Milestones was considered normal. On admission, his oxygen saturation was 88% with ambient air. The diagnosis was confirmed by echocardiography. He was planned to undergo staging surgery which would end to Fontan Procedure. Pulmonary Artery (PA) banding was performed to reduce blood flow to pulmonary circulation, distribute more blood from the left ventricle to aorta and systemic circulation and prepare for bidirectional Glenn Shunt procedure one year later and Fontan procedure a year after that.
Khairy P, Poirer N, Mercie LA. Univentricular Heart.Circulation.2007; 115:800-812.
Children’s Hospital and Clinic Minnesota. 2012. Available from:
Kaneshiro NK. Double Inlet Left Ventricle.2012. Available from:
The Royal Children’s Hospital Medicine. Double Inlet Left Ventricle (DILV). Available from : http://www.rch.org.au/cardiologyheart_defects/Double_Inlet_Left_Ventricle_DILV/
Hok KC, Jieh NW, Wen PH, Wen LY, Jing MW. Double-
Outlet Left Ventricle with Ebstein Anomaly in a Neonate with VACTERL Association. Acta Cardiol Sin 2011;27:65_7
Vyas H, Hagler DJ. Double Inlet Left Ventricle. Current Treatment Options in Cardiovascular Medicine 2007;9: 391-398.
Kanakis MA, Petropoulos AC, Mitropolus F. Fontan Operation. Hellenic J Cardiol 2009; 50: 133-141.
Gewillig M. The Fontan Circulation. Heart 2005;91:839–
Bhimji S. Pulmonary artery banding. Available from: http://emedicine.medscape.com/article/905353-overview
Pelletier G, Jacobs M. Superior Cavopulmonary Anastomosis: The Hemi-Fontan and Bidirectional Glenn. 2013. Available from: http://www.ctsnet.org/sections/clinicalresources/congenital/expert_tech-6