Rhabdomyoma Penyebab Obstruksi Ventrikel Kiri Pada Neonatus Umur Dua Hari

  • S Suryono Department of Cardiology and Vascular Medicine
  • Mahrus A Rachman Subdivision of Cardiology Depart-ment of Child Health Airlangga University Medical School – Dr Soetomo Hospital Surabaya
  • Teddy Ontoseno Subdivision of Cardiology Depart-ment of Child Health Airlangga University Medical School – Dr Soetomo Hospital Surabaya

Abstract

Tumor intrakardiak pada pediatri sangat jarang ditemukan, kejadiannya hanya mencapai 0,001% sampai 0,003% dari semua kasus yang diterima di rumah sakit rujukan. Rhabdomyomamerupakan tumor jinak intrakardiak yang ditemukan pada bayi di bawah usia satu tahun, kejadiannya mencapai lebih dari 75% dari keseluruhan kasus tumor jantung dengan distribusi sama antara pria dan wanita.
Rhabdomyomabiasanya multiple, berukuran antara beberapa millimeter hingga beberapa sentime-ter; lokasinya dapat intramural pada dinding, septum bahkan pada rongga ventrikel. Gambaran klinisnya dapat berupa : obstruksi ventrikel, aritmia dan kematian mendadak.
Obstruksi ventrikel kiri (left ventricle/LV) yang ditandai dengan gagal jantung merupakan mani-festasi klinis Rhabdomyomayang sangat langka.
Diagnosis dini tumor jantung (Rhabdomyoma) pada LV merupakan hal penting karena tindakan be-dah diharapkan dapat memberikan perbaikan klinis dan harapan hidup lebih panjang, meskipun reseksi sempurna tidak selalu tercapai.

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How to Cite
Suryono, S., Rachman, M., & Ontoseno, T. (1). Rhabdomyoma Penyebab Obstruksi Ventrikel Kiri Pada Neonatus Umur Dua Hari. Indonesian Journal of Cardiology, 29(1), 40-6. https://doi.org/10.30701/ijc.v29i1.201
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Case Reports