Rhabdomyoma Penyebab Obstruksi Ventrikel Kiri Pada Neonatus Umur Dua Hari
Abstract
Tumor intrakardiak pada pediatri sangat jarang ditemukan, kejadiannya hanya mencapai 0,001% sampai 0,003% dari semua kasus yang diterima di rumah sakit rujukan. Rhabdomyomamerupakan tumor jinak intrakardiak yang ditemukan pada bayi di bawah usia satu tahun, kejadiannya mencapai lebih dari 75% dari keseluruhan kasus tumor jantung dengan distribusi sama antara pria dan wanita.Rhabdomyomabiasanya multiple, berukuran antara beberapa millimeter hingga beberapa sentime-ter; lokasinya dapat intramural pada dinding, septum bahkan pada rongga ventrikel. Gambaran klinisnya dapat berupa : obstruksi ventrikel, aritmia dan kematian mendadak.
Obstruksi ventrikel kiri (left ventricle/LV) yang ditandai dengan gagal jantung merupakan mani-festasi klinis Rhabdomyomayang sangat langka.
Diagnosis dini tumor jantung (Rhabdomyoma) pada LV merupakan hal penting karena tindakan be-dah diharapkan dapat memberikan perbaikan klinis dan harapan hidup lebih panjang, meskipun reseksi sempurna tidak selalu tercapai.
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References
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Fyler DC. Cardiac tumors. In: Fyler DC, editor. Nadas’ Pediatric Cardiology. Philadelphia: Hanley and Belfus; 1992. p. 727-30
Darling TN. Tuberous Sclerosis Complex. In : Wolf K, Gold-smith LA, Stephen IK, Gilchrest B, Paller A, Leffell DJ, editors. Fitzpatrick’s Dermatology in general Medicine. 7th ed. New York: Mc.Graw-Hill; 2008. p. 1327-30
Marx GR, Moran MA. Cardiac tumors. In : Allen HD, Gut- In : Allen HD, Gut-gesell HP, Clark EB, editors. Moss and Adams’ Heart Disease in Infant, Children and Adolescents. 6th edition. Philadelphia: Lippincott Williams and Wilkins; 2000.p.1435-7
Ibrahim CPH, Thakker P, Miller PA, Barron D. Cardiac rhab-domyoma presenting as left ventricular outflow tract obstruction in a neonate. Interactive Cardiovascular and Thoracic surgery 2. 2003. 573-4
Miner S, Abramowitz JA, Levin SE. Rhabdomyoma of the Heart in a new-born infant diagnosis by echocardiography. Br Heart J 1980; 44: 224-7
Erdem S, Kucukosmanoglu O et al. A Case Report: Rhab- A Case Report: Rhab-domyoma Caused Right Ventricular Outflow Tract Obstruction in an Infant
Geva T, Santini F, Pear W at al. Cardiac Rhabdomyoma. Rare cause of Fetal Death. American College of Chest Physicians. 1991. 139-42
Feigenbaum H, Armstrong W, Ayan T. In Feigenbaum’s Echocardiography 6th edition. Philadelphia: Lippincott Williams and Wilkins; 2000.p. 710-18
Farooki ZQ, Ross RD at al. Spontaneous regression of cardiac rhabdomyoma. AM J Cardiol 1991; 67:897-9
Ross RD, Farooki ZQ. Medical versus surgical management of intracardiac rhabdomyoma. Am J Cardiol 1991; 68: 836
Fyler DC. Cardiac tumors. In: Fyler DC, editor. Nadas’ Pediatric Cardiology. Philadelphia: Hanley and Belfus; 1992. p. 727-30
Darling TN. Tuberous Sclerosis Complex. In : Wolf K, Gold-smith LA, Stephen IK, Gilchrest B, Paller A, Leffell DJ, editors. Fitzpatrick’s Dermatology in general Medicine. 7th ed. New York: Mc.Graw-Hill; 2008. p. 1327-30
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How to Cite
Suryono, S., Rachman, M., & Ontoseno, T. (1). Rhabdomyoma Penyebab Obstruksi Ventrikel Kiri Pada Neonatus Umur Dua Hari. Indonesian Journal of Cardiology, 29(1), 40-6. https://doi.org/10.30701/ijc.v29i1.201
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Case Reports
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