Diagnosis Sindrom Brugada
Abstract
Brugada syndrome is an inherited autosomal dominant disease that cause sudden death, which related with mutation of SCN5A gene, ? subunit of sodium channel. The risk Brugada syndrome in male is 8 times more than females. The average age is 40 years old, which can happen between age 1 to 77 years old. The Incidence is 5 to 66 per 10.000 people. The golden diagnostic tools is ECG, an abnormality QRS-T found in lead V1-V3. I report a case of Brugada syndrome with neither sign nor symptoms. The disease coincidental in routine medical examination.Downloads
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References
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2. Priori SG, Wilde AA, Horie M, Cho Y, Behr ER, Berul C, et al. Executive Summary: HRS/EHRA/APRHRS expert consensus statement on the diagnosis and management of patients with inherited primary arrthmia syndrome. Europace. 2013; 15: 1389-1406.
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4. Wilde AM, Anzelevitch C, Boggrefe M, Brugada J, Brugada R, Brugada P, et al. Proposed Diagnostic Criteria for the Brugada Syndrome: Consensus Report. Circulation. 2012; 106: 2514-2519.
5. Mizusawa Y, Wilde AAM. Brugada Syndrome. Circ Arrhythm Electrophysiol. 2012; 5: 606-616.
6. Luna ABD, Brugada J, Baranchuk A, Bogreffe M, Breithardt G, Goldwasser D, et al. Current Electrocardiographic Criteria for diagnosis of Brugada pattern: a consensus report. Journal of Electrocardiology. 2012; 45: 433-442.
7. Chen PS, Priori SG. The Brugada Syndrome. JACC. 2008; 51: 1176-80.
8. Meregalli PG, Wilde AAM, Tan HL. Review Pathophysiological Mechanism of Brugada Syndrome: Depolarization disorder, repolarization disorder, or more? Cardiovascular Research. 2005; 67: 367-378.
9. Aizawa Yoshiyasu, Kimura Takehiro, and Seiji Takatsuki. EP Case Report: A Case of Brugada Syndrome Showing Augmentation of Electrocardiogram Phenotype by Complete Bundle Branch Block. Europace. 2013; doi: 10.1093/europace/eut 219.
2. Priori SG, Wilde AA, Horie M, Cho Y, Behr ER, Berul C, et al. Executive Summary: HRS/EHRA/APRHRS expert consensus statement on the diagnosis and management of patients with inherited primary arrthmia syndrome. Europace. 2013; 15: 1389-1406.
3. Anzelevitch et al. Issue Highlights. Function Mutations in The Cardiac Calcium Channel Underline A New Clinical Entity Characterized by ST-Segment Elevation, Short QT Intervals, and Sudden Cardiac Death. Circulation. 2007; 115: 13f-16f.
4. Wilde AM, Anzelevitch C, Boggrefe M, Brugada J, Brugada R, Brugada P, et al. Proposed Diagnostic Criteria for the Brugada Syndrome: Consensus Report. Circulation. 2012; 106: 2514-2519.
5. Mizusawa Y, Wilde AAM. Brugada Syndrome. Circ Arrhythm Electrophysiol. 2012; 5: 606-616.
6. Luna ABD, Brugada J, Baranchuk A, Bogreffe M, Breithardt G, Goldwasser D, et al. Current Electrocardiographic Criteria for diagnosis of Brugada pattern: a consensus report. Journal of Electrocardiology. 2012; 45: 433-442.
7. Chen PS, Priori SG. The Brugada Syndrome. JACC. 2008; 51: 1176-80.
8. Meregalli PG, Wilde AAM, Tan HL. Review Pathophysiological Mechanism of Brugada Syndrome: Depolarization disorder, repolarization disorder, or more? Cardiovascular Research. 2005; 67: 367-378.
9. Aizawa Yoshiyasu, Kimura Takehiro, and Seiji Takatsuki. EP Case Report: A Case of Brugada Syndrome Showing Augmentation of Electrocardiogram Phenotype by Complete Bundle Branch Block. Europace. 2013; doi: 10.1093/europace/eut 219.
Published
2015-05-08
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How to Cite
Faisal, E. (2015). Diagnosis Sindrom Brugada. Indonesian Journal of Cardiology, 35(2), 96-101. https://doi.org/10.30701/ijc.v35i2.397
Section
Case Reports
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