Lutembacher’s Syndrome An Echocardiographic Assessment
Abstract
Lutembacher’s syndrome (LS), consisted of Atrial Septal Defect(ASD) and Mitral Stenosis (MS), is a very rare form of cardiac anomaly. Rene Lutembacher’s first described this syndrome in 1916. Currently, any combination of ASD, congenital or iatrogenic and MS, acquired or congenital is referred as LS.By using echocardiography, the hemodynamic of LS could be assesed. Pathophysiologically, the hemodynamic of ASD is related to the magnitude and direction of shunting across the interatrial communication. The determinants of the amount of shunting are the defect size and theventricles relative resistance to inflow. In MS, the restricted in?low leads to increased
diastolic pressures in the left ventricle. This resulted in marked accentuation of the left-to-right shunt.
We reported a case of a 34 years old female, first came to Harapan Kita National Cardiac Center, in 2010. She was diagnosed with LS, and was planned to have ASD closure and mitral valve repair by surgery. However, she refused to undertake the procedure.
In summary, to illustrate the interactions between ASD and MS, the presence of ASD underestimated the severi?y of MS; meanwhile the existence of MS magnified the left to right shunt in patients with ASD.
Downloads
Download data is not yet available.
References
Besterman E. Atrial Septal Defect with Pulmonary Hypertension. British Heart Journal. 1961.
Ahmed WH, Al-Shaibi KF, Chamsi-Pasha H, Abdelmenem A. Non-surgical correction of Lutembacher syndrome. Saudi Med J. 2003 Mar;24(3):307-8.
Crawford M. Iatrogenic’s Lutembacher’s Syndrome Revisited. Circulation. 1990;81(2):1422-4.
Muhammad Ashiqur Rahman AFR, Tauhidul Haque, Sajal K Banarjee, Md. Harisul Hoque, Md. Ashraf Uddin Sultan. A Forty Year Old Lady with Undiagnosed Lutembacher Syndrome — A Case Report. University Heart Journal. 2010;6(1):51-5.
David H. Adams TMB, Helmet Baumgartner, Michael A. Beardslee, Ronen Beeri, Peter C. Block. Valvular Heart Disease: A Companion to Braunwald’s Heart Disease. Philadelphia: Saunders and Elseviers; 2009.
Solomon SD. Essential Echocardiography: A Practical Hand-book. New Jersey: Humana Press; 2007.
Pravin M. Shah MDF, Bruce W. Lytle, Patrick T. O’Gara, Robert A. O’Rourke, and Shah, Jack S. Shanewise, Rick A. Nishimura, Blase A. Carabello, David P. Faxon, Nishimura, Patrick T. O’Gara, Robert A. O’Rourke, Catherine M. Otto, Pravin M. David P. Faxon, Michael D. Freed, William H. Gaasch, Bruce W. Lytle, Rick A. ACC/AHA 2008 Guidelines for the Manage-ment of Patients With Valvular Heart Disease:. Journal of The American College of Cardiology. 2008;52(142):1-145.
Anderson RH. Pediatric Cardiology. Philadelphia: Churchill Lvingstone; 2010.
Chau EM, Lee CH, Chow WH. Transcatheter treatment of a case of Lutembacher syndrome. Catheter Cardiovasc Interv. 2000 May;50(1):68-70.
Chi-Lin Ho K-WL, Yun-Ching Fu, Sheng-Ling Jan, Ming-Chi Lin, Ching-Shiang Chi, Betau Hwang. Transcath-eter Therapy of Lutembacher Syndrome. Chin Med J (Engl). 2007;70(6):253-6.
Mostafa Behjatiardakani MR, Hossein Nough, and Reza Rafiei. Trans-Catheter Therapy of Lutembacher Syndrome: A Case Report. Acta Medica Iranica. 2009;49(5):325-9
Ahmed WH, Al-Shaibi KF, Chamsi-Pasha H, Abdelmenem A. Non-surgical correction of Lutembacher syndrome. Saudi Med J. 2003 Mar;24(3):307-8.
Crawford M. Iatrogenic’s Lutembacher’s Syndrome Revisited. Circulation. 1990;81(2):1422-4.
Muhammad Ashiqur Rahman AFR, Tauhidul Haque, Sajal K Banarjee, Md. Harisul Hoque, Md. Ashraf Uddin Sultan. A Forty Year Old Lady with Undiagnosed Lutembacher Syndrome — A Case Report. University Heart Journal. 2010;6(1):51-5.
David H. Adams TMB, Helmet Baumgartner, Michael A. Beardslee, Ronen Beeri, Peter C. Block. Valvular Heart Disease: A Companion to Braunwald’s Heart Disease. Philadelphia: Saunders and Elseviers; 2009.
Solomon SD. Essential Echocardiography: A Practical Hand-book. New Jersey: Humana Press; 2007.
Pravin M. Shah MDF, Bruce W. Lytle, Patrick T. O’Gara, Robert A. O’Rourke, and Shah, Jack S. Shanewise, Rick A. Nishimura, Blase A. Carabello, David P. Faxon, Nishimura, Patrick T. O’Gara, Robert A. O’Rourke, Catherine M. Otto, Pravin M. David P. Faxon, Michael D. Freed, William H. Gaasch, Bruce W. Lytle, Rick A. ACC/AHA 2008 Guidelines for the Manage-ment of Patients With Valvular Heart Disease:. Journal of The American College of Cardiology. 2008;52(142):1-145.
Anderson RH. Pediatric Cardiology. Philadelphia: Churchill Lvingstone; 2010.
Chau EM, Lee CH, Chow WH. Transcatheter treatment of a case of Lutembacher syndrome. Catheter Cardiovasc Interv. 2000 May;50(1):68-70.
Chi-Lin Ho K-WL, Yun-Ching Fu, Sheng-Ling Jan, Ming-Chi Lin, Ching-Shiang Chi, Betau Hwang. Transcath-eter Therapy of Lutembacher Syndrome. Chin Med J (Engl). 2007;70(6):253-6.
Mostafa Behjatiardakani MR, Hossein Nough, and Reza Rafiei. Trans-Catheter Therapy of Lutembacher Syndrome: A Case Report. Acta Medica Iranica. 2009;49(5):325-9
Views & Downloads
Abstract views: 2919
PDF downloads: 2869
PDF downloads: 2869
How to Cite
Fahmi, M., Mardiani, A., & Harimurti, G. (1). Lutembacher’s Syndrome An Echocardiographic Assessment. Indonesian Journal of Cardiology, 33(2), 99-105. https://doi.org/10.30701/ijc.v33i2.60
Section
Case Reports
Authors who publish with this journal agree to the following terms:
- Authors retain copyright and grant the journal right of first publication with the work simultaneously licensed under a Creative Commons Attribution License that allows others to share the work with an acknowledgement of the work's authorship and initial publication in this journal.
- Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journal's published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgement of its initial publication in this journal.
- Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work (See The Effect of Open Access).
